Juvenile dermatomyositis

juvenile dermatomyositis: Juvenile dermatomyositis (JDM) is the early-onset form of dermatomyositis (DM, see this term), a systemic, autoimmune inflammatory muscle disorder, characterized by proximal muscle weakness, evocative skin lesion, and systemic manifestations.

Endpoint definition

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FinnGen phenotype data
diagram bullet diagram downward connector

Filter registries Inpat., Oupat., Death

Hospital Discharge: ICD-10 M33.0
Hospital discharge: ICD-9 7103A
Cause of death: ICD-10 M33.0
Cause of death: ICD-9 7103A

Check pre-conditions None

Include endpoints None

Check conditions None

Apply sex-specific rule None

diagram downward connector M13_JUVDERMATOMYO

Extra metadata

Level in the ICD hierarchy 4
First used in FinnGen datafreeze DF2
Parent code in ICD-10 M33
Name in latin Dermatomyositis juvenilis

Summary Statistics

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Key figures

All Female Male
Number of individuals 27 15 12
Unadjusted prevalence (%) 0.01 0.01 0.01
Mean age at first event (years) 33.27 26.97 41.13

Mortality

Follow-up Absolute risk HR [95% CI] p N
1998–2019 - - - -
15 years - - - -
5 years - - - -
1 year - - - -

Correlations

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Index endpoint: M13_JUVDERMATOMYO – Juvenile dermatomyositis
GWS hits:

Survival analyses between endpoints

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Plot

before Juvenile dermatomyositis
after Juvenile dermatomyositis

loading spinner Loading survival analyses plot

Drugs most likely to be purchased after Juvenile dermatomyositis

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